Dr.Nikhila Sai Nallapati

Dr.Viswamithra Penumala, Dr.Hema Sai Gongati, Dr.Rishitha Srinidhi Boddu

Abstract

Iridocorneal endothelial syndrome(ICE) is a unique ophthalmic disorder that involves an irregular corneal endothelium that can lead to varying degrees of corneal edema, iris atrophy, and secondary angle closure glaucoma. It is sporadic in presentation, usually unilateral and typically affect adult patients, females more often than males. Prevalence is less than one per two lakh population. It has three clinical entities-Chandler's syndrome, Progressive iris atrophy, Cogan Reese syndrome. We report a case of 42 year old female who presented to our hospital with a chief complaint of loss of vision in left eye since many years. On examination she had no perception of light in left eye and intraocular pressure is recorded to be 38mm hg. Several iris atrophic patches with iris holes were present. Mild corneal edema was present. Pupil had corectopia. Fundus examination revealed 0.8 CDR with macular dystrophy.